![]() ![]() Once the diagnosis of Robin sequence is made other adjuncts such as an associated cleft palate, syndrome or feeding problems could be added to the description. We suggest using the description originally summarised by Pierre Robin consisting of micrognathia, glossoptosis and airway compromise. The treatment of patients with Robin sequence often involves multidisciplinary involvement, making it crucial to have one common definition. This lack of uniformity in the definition hampers the comparison of outcome studies. ![]() One study showed an average of 83 hearing loss in PRS, compared to 60 in cleft individuals without PRS (Handzic et al., 1995). Our study demonstrates that there is widespread confusion in the Netherlands defining Robin sequence. Persons with Pierre Robin sequence (PRS) are at greater risk for hearing impairment than persons with cleft lip and/or palate without PRS. Specific syndromes in which craniofacial abnormalities are the primary feature will be reviewed here. Sixty-six questionnaires were returned, demonstrating 29 different descriptions. Craniofacial surgery, which consists of reconstruction of the cranial vault and/or facial skeleton with or without simultaneous soft tissue reconstruction, can be performed when these deformities interfere with physical and/or mental well-being. At our Annual Dutch Cleft Palate Meeting a questionnaire was given to all those attending requesting them to summarise characteristics needed for a definition of 'Robin sequence'. This prompted us to perform a review into the current understanding when diagnosing and defining this disorder. Pierre Robin sequence (PRS) is defined by 3 related findings: micrognathia, glossoptosis, and tongue-based airway obstruction (TBAO). Ryan (B&B) mentioned airway obstruction when talking about treacher collins. so how can I differentiate between them FA has airway obstruction under pierre robin but Dr. While reviewing treatment options for Robin sequence we were surprised to see how often different definitions were used to describe this condition. Pierre Robin vs Treacher collins FA says these are both abnormalities within the 1st branchial arch, and they're both similar (small jaw and other features). Defining this disorder correctly has important consequences for physicians and parents. Different nosology has hampered our understanding of patients with Robin sequence. ![]()
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